Search on: METHYLMALONYL-COA DECARBOXYLASE 
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Descriptor English:   Methylmalonyl-CoA Decarboxylase 
Descriptor Spanish:   Metilmalonil-CoA Descarboxilasa 
Descriptor Portuguese:   Metilmalonil-CoA Descarboxilase 
Synonyms English:   Propionyl-CoA Carboxylase  
Tree Number:   D08.811.520.224.125.387
Definition English:   A carboxy-lyase that catalyzes the decarboxylation of (S)-2-Methyl-3-oxopropanoyl-CoA to propanoyl-CoA. In microorganisms the reaction can be coupled to the vectorial transport of SODIUM ions across the cytoplasmic membrane. 
Entry Combination - descr/qualif English:   Methylmalonyl-CoA Decarboxylase/deficiency use Propionic Acidemia
 
See Related English:   Propionic Acidemia
 
History Note English:   2004; use METHYLMALONYL-COA DECARBOXYLASE (NM) 1980-2003 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DU diagnostic use
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
SE secretion ST standards
SD supply & distribution TU therapeutic use
TO toxicity UL ultrastructure
UR urine  
Record Number:   38186 
Unique Identifier:   D043586 

Occurrence in VHL:
 

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